Hypertrophic cardiomyopathy (HCM) is one of the common cardiomyopathies in cardiology practice known by a characteristic involvement of the left ventricle. We report a rare and intriguing case of severe HCM with right ventricle involvement in a child.

Hypertrophic cardiomyopathies in children cover a much greater semiological, sonographic and etiological diversity than that of adults. In paediatrics, emphasis should be placed on etiological investigation. These patients must be cared for in highly specialized centers with expertise not only in cardiopediatrics but also in metabolic pediatrics and genetics.